Primary Squamous Cell Carcinoma (SCC) of the Kidney is a rare variety of Renal Cell Carcinoma. Patients present with inconclusive signs and symptoms and thus diagnosis is unsuspected. Therefore, these patients land in advanced stage disease and have poor prognosis. Here we present a Case of Squamous Cell Carcinoma Kidney, who presented in advanced stage, his workup and the treatment done. A 52-year-old male presented with left flank pain and fever. A computerized tomography (CT) scan showed nephrolithiasis and chronic inflammation in the left kidney and a soft tissue heterogenously enhancing lesion at the upper pole causing hydronephrosis . He underwent Radical Nephrectomy and Histopathological examination revealed an invasive, moderately differentiated squamous cell carcinoma involving renal parenchyma, perinephric tissue, fat and hilar lymph nodes (stage 3). Thereafter, patient was treated with Radiotherapy and Chemotherapy ,then he was planned for metronomic chemotherapy. Primary Renal squamous cell carcinomas are very rare tumours which are often not clinically suspected or diagnosed. These tumours require thorough clinical examination, radiological workup, aggressive approach towards treatment to add years in their life owing to worse prognosis and highly proliferative variety of the primary.