In the present case report we describe a rare case of a 3-year-old male patient with a history of absence of both eyeball since birth now presenting with tender cystic swelling of right lower preseptal and orbital area with discolouration of the skin. There is history of intermittent discharge since 1 year. This case report highlights the step wise approach to diagnose a case of bilateral anophthalmia presenting with lymphangioma of bilateral orbit and its management by percutaneous sclerotherapy with injection bleomycin leading to promising results.