Klippel Trenaunay Weber Syndrome (KTWS) is a rare, sporadic, complex manifestation characterised by micro arteriovenous and capillary malformation, along with varicose veins and bony and/or soft tissue hypertrophy. The vascular malformation are usually limited to single extremity and affected limb has cutaneous flush involving skin and is increased in length and girth. Patients can have visceral organ complications that are very dreadful complications of the syndrome. Treatment is normally cautious, regular follow-up for progression is advised. There are very limited case reports available on this rare syndrome.